Poland Syndrome: A Case Study

Authors

  • Naveen Reddy MV
  • Rupa Reddy M

Abstract

We report a rare case of Poland syndrome in a 22-year-old female patient. This is a syndrome defined bytheunilateral absence or hypoplasia of the thoracic muscles with under development of one breast. A female patient presented with aesthetic concerns having hypoplasia of left breast and the nipple-areola complex small and displaced laterally. There were no other developmental problems with ribs, breast bone or upper extremity. The patient was surgically treated with breast reconstruction using amammary prosthesis. The incidence of Poland syndrome ranges from 1 in 7000 to 1 in 1,00,000 [Fokin and Robicsek (2002). Ann Thorac Surg 2002;74(6):2218–25]. Ten percent of these patients also express some of the other features of the disorder. There is a male to female ratio of 2:1 to 3:1.

References

Fokin A, Robicsek F. Poland’s syndrome revisited. Ann Thorac Surg 2002;74(6):2218–25.

Poland A. Deficiency of the pectoral muscles. Guy’s Hospital Rep 1841;VI:191–3.

Poullin P, Toussirot E, Schiano A, Serratrice G. Complete and dissociated forms of Poland’s syndrome (5 cases). Rev Rhum Mal Osteoartic 1992;59(2):114–20.

Samuels TH, Haider MA, Kirbride P. Poland’s syndrome: a mammographic presentation. AJRAMJ Roentgenol 1996;116(2):247–8.

Je5. Mi-Young Jeung, MD, Afshin Gangi, MD, PhD, Bernard Gasser, MD, Cornelia Vasilescu, MD, Gilbert Massard, MD, Jean-Michel Wihlm, MD, Roy C. Imaging of chest wall disorders. Radiographics. 1999,19(3):617-37

Cingel V, Bohac M, Mestanova V, Zabojnikova L, VargaI. Poland syndrome: from embryological basis to plastic surgery. Surg Radiol Anat 2013; 35(8):639–46. doi: 10.1007/s00276-013-1083-7. E pub 2013 Feb 19. Review.

Seyfer AE, Fox JP, Hamilton CG. Poland syndrome: evaluation and treatment of the chest wall in 63 patients. Plast Reconstr Surg 2010;126(3):902–11.

Downloads

Published

2015-05-27

Issue

Section

Case Report